5A70, 5A71, 5A72, 5A73, 5A74, 5A75, 5A76

Disorders Of The Adrenal Glands Or Hormones – ICD 11 Codes

Coded Elsewhere:

Cushing syndrome

Cushing syndrome results from excess of corticosteroid hormones in the body due to overstimulation of the adrenal glands by excessive amounts of the hormone ACTH, secreted either by a tumuor of the pituitary gland (Cushing’s disease) or by a malignant tumour in the lung or elsewhere. Symptoms include weight gain, reddening of the face and neck, excess growth of body and facial hair, raised blood pressure, loss of mineral from the bones (osteoporosis), raised blood glucose levels, and sometimes mental disturbances.

ICD 11 Code For Cushing syndrome

  5A70  Cushing syndrome

5A70.0 Pituitary-dependent Cushing disease

Definition of Pituitary-dependent Cushing disease: Pituitary-dependent Cushing disease is caused by a pituitary tumour, generally benign (adenoma) but rarely malignant (carcinoma), which secretes adrenocorticotropin (ACTH) autonomously, leading to hypercortisolism. The condition is associated with increased morbidity and mortality that can be mitigated by treatments that result in sustained endocrine remission. Transsphenoidal pituitary surgery (TSS) remains the mainstay of treatment for this disease but requires considerable neurosurgical expertise and experience in order to optimize patient outcomes.

5A70.1 Ectopic ACTH syndrome

5A70.2 Pseudo-Cushing syndrome

Definition of Pseudo-Cushing syndrome: This is a condition in which patients display the signs, symptoms, and abnormal hormone levels seen in Cushing’s syndrome. However, pseudo-Cushing’s syndrome is not caused by a problem with the hypothalamic-pituitary-adrenal axis as Cushing’s is; it is an idiopathic condition.

5A70.3 Nelson syndrome

5A70.Y Other specified Cushing syndrome

5A70.Z Cushing syndrome unspecified

Definition of Adrenogenital disorders: Disorders of the reproductive system resulting from pathologic androgen production secondary to abnormalities in cortisol and/or aldosterone production

  5A71  Adrenogenital disorders

5A71.0 46 XX disorders of sex development induced by androgens of fetal origin

Definition of 46 XX disorders of sex development induced by androgens of fetal origin: This refers to 46 XX disorders of sex development induced by any natural or synthetic compound, usually a steroid hormone, that stimulates or controls the development and maintenance of male characteristics in vertebrates by binding to androgen receptors, of fetal origin.

5A71.00 Glucocorticoid resistance

Definition of Glucocorticoid resistance: Glucocorticoid resistance is a rare genetic endocrine condition characterised by generalised, partial, target tissue resistance to glucocorticoids. The clinical spectrum of the condition is broad, ranging from asymptomatic to severe cases of hyperandrogenism, fatigue and/or mineralocorticoid excess.

5A71.01 Congenital adrenal hyperplasia

Definition of Congenital adrenal hyperplasia: Congenital adrenal hyperplasia (CAH) refers to a group of conditions associated with either complete (classical form) or partial (non-classical) anomalies in the biosynthesis of adrenal hormones. The condition is characterised by insufficient production of cortisol, or of aldosterone (classical form with salt wasting), associated with overproduction of adrenal androgens. In the classical form, metabolic decompensation (dehydration with hyponatraemia, hyperkalaemia and acidosis associated with mineralocorticoid deficiency, and hypoglycaemia associated with glucocorticoid deficiency) may be life-threatening from the neonatal period onwards. Genital variations may be noted at birth in affected females. Chronic hyperandrogenism may lead to accelerated growth during childhood, but advanced bone maturation may lead to a deficit in final height. Adults tend to be overweight and metabolic disturbances, bone anomalies and fertility problems may also be present. Non-classical forms are associated with later onset, during the peri- or postpubertal period, and manifest with signs of hyperandrogenism (acne, hirsutism, menstrual problems and infertility).

5A71.0Y Other specified 46 XX disorders of sex development induced by androgens of fetal origin

5A71.0Z 46 XX disorders of sex development induced by androgens of fetal origin unspecified

5A71.1 46 XX disorders of sex development induced by androgens of maternal origin

Definition of 46 XX disorders of sex development induced by androgens of maternal origin: This refers to 46,XX disorders of sex development induced by any natural or synthetic compound, usually a steroid hormone, that stimulates or controls the development and maintenance of male characteristics in vertebrates by binding to androgen receptors, of maternal origin.

5A71.Y Other specified adrenogenital disorders

5A71.Z Adrenogenital disorders unspecified

Hyperaldosteronism

ICD 11 Code For Hyperaldosteronism

  5A72  Hyperaldosteronism

5A72.0 Primary hyperaldosteronism

5A72.1 Secondary hyperaldosteronism

Coding Note:

  • Code also the causing condition

5A72.Z Hyperaldosteronism unspecified

Hypoaldosteronism

ICD 11 Codes For Hypoaldosteronism

  5A73  Hypoaldosteronism

Exclusions:

  • Congenital adrenal hyperplasia (5A71.01)

Adrenocortical insufficiency

Definition of Adrenocortical insufficiency: A condition in which the adrenal glands do not produce adequate amounts of steroid hormones, primarily cortisol. It may also include impaired production of aldosterone (a mineralocorticoid), which regulates sodium conservation, potassium secretion, and water retention and also accompanies impaired production of adrenal androgens.

ICD 11 Code For Adrenocortical insufficiency

  5A74  Adrenocortical insufficiency

Coded Elsewhere:

  • X-linked adrenoleukodystrophy (5C57.1)

5A74.0 Acquired adrenocortical insufficiency

Definition of Acquired adrenocortical insufficiency: This is a acquired condition in which the adrenal glands do not produce adequate amounts of steroid hormones, primarily cortisol; but may also include impaired production of aldosterone (a mineralocorticoid), which regulates sodium conservation, potassium secretion, and water retention.

Exclusions:

Coded Elsewhere:

5A74.1 Adrenal crisis

Definition of Adrenal crisis: Adrenal crisis is a life-threatening condition that indicates severe adrenal insufficiency caused by insufficient levels of cortisol.

Coded Elsewhere:

  • Waterhouse-Friderichsen syndrome (1C1C.1)

5A74.Y Other specified adrenocortical insufficiency

5A74.Z Adrenocortical insufficiency unspecified

Adrenomedullary hyperfunction

Definition of Adrenomedullary hyperfunction: Idiopathic overstimulation of the adrenal medulla resulting in pathologic epinephrine/norepinephrine-mediated sympathetic output

ICD 11 Code For Adrenomedullary hyperfunction

  5A75  Adrenomedullary hyperfunction

Certain specified disorders of adrenal gland

ICD 11 Code For Certain specified disorders of adrenal gland

  5A76  Certain specified disorders of adrenal gland

5A76.0 Premature adrenarche

Definition of Premature adrenarche: Premature development of pubic and/or axillary hair without central or peripheral precocious puberty. Children show premature clinical and/or laboratory signs of androgen action without estrogen action.

Exclusions:

5A76.Y Other specified disorders of adrenal gland

Disorders of the adrenal glands or adrenal hormone system unspecified

ICD 11 Code For Disorders of the adrenal glands or adrenal hormone system unspecified

  5A7Z  Disorders of the adrenal glands or adrenal hormone system unspecified

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