Immune System Disorders Involving White Cell Lineages – ICD 11 Codes
Coded Elsewhere:
- Immunodeficiencies with predominantly antibody defects (4A01.0)
- Combined immunodeficiencies (4A01.1)
- Defects in the complement system (4A00.1)
- Diseases of immune dysregulation (4A01.2)
- Other well-defined immunodeficiency syndromes due to defects in adaptive immunity (4A01.3)
Disorders of neutrophil number
ICD 11 Code For Disorders of neutrophil number
4B00 Disorders of neutrophil number
Exclusions:
- Decreased white blood cell count (MA16.10)
4B00.0 Neutropaenia
Coded Elsewhere:
- Transient neonatal neutropaenia (KA8D)
4B00.00 Constitutional neutropaenia
Definition of Constitutional neutropaenia: This is a granulocyte disorder characterised by an abnormally low number of neutrophils. Neutrophils usually make up 50-70% of circulating white blood cells and serve as the primary defence against infections by destroying bacteria in the blood.
Exclusions:
- Cartilage-hair hypoplasia (LD27.0)
4B00.01 Acquired neutropaenia
4B00.0Z Neutropenia unspecified
4B00.1 Neutrophilia
4B00.10 Constitutional neutrophilia
4B00.11 Acquired neutrophilia
Coding Note:
- Code also the causing condition
Exclusions:
- Non mast cell myeloproliferative neoplasms (2A20)
4B00.1Z Neutrophilia unspecified
4B00.Y Other specified disorders of neutrophil number
Disorders of neutrophil function
ICD 11 Code For Disorders of neutrophil function
4B01 Disorders of neutrophil function
Coded Elsewhere:
- Functional neutrophil defects (4A00.0)
4B01.0 Constitutional disorders of neutrophil function
4B01.00 Disorders of neutrophil adhesion
4B01.01 Disorders of neutrophil chemotaxis
4B01.02 Disorders of neutrophil granule formation or release
4B01.03 Disorders of neutrophil oxidative metabolism
4B01.0Y Other specified constitutional disorders of neutrophil function
4B01.0Z Constitutional disorders of neutrophil function unspecified
4B01.1 Acquired disorders of neutrophil function
4B01.Z Disorders of neutrophil function unspecified
Eosinopenia
ICD 11 Code For Eosinopenia
4B02 Eosinopenia
4B02.0 Constitutional decrease in eosinophil number
4B02.1 Acquired decrease in eosinophil number
4B02.Z Eosinopenia unspecified
Eosinophilia
ICD 11 Code For Eosinophilia
4B03 Eosinophilia
4B03.0 Constitutional eosinophilia
4B03.1 Acquired eosinophilia
4B03.Z Eosinophilia unspecified
Disorders with decreased monocyte counts
ICD 11 Code For Disorders with decreased monocyte counts
4B04 Disorders with decreased monocyte counts
Disorders with increased monocyte counts
ICD 11 Code For Disorders with increased monocyte counts
4B05 Disorders with increased monocyte counts
Acquired lymphopenia
ICD 11 Code For Acquired lymphopenia
4B06 Acquired lymphopenia
Acquired lymphocytosis
ICD 11 Code For Acquired lymphocytosis
4B07 Acquired lymphocytosis
Exclusions:
- Chronic lymphocytic leukaemia or small lymphocytic lymphoma (2A82.0)
Coded Elsewhere:
- Infectious mononucleosis (1D81)
Other specified immune system disorders involving white cell lineages
ICD 11 Code For Other specified immune system disorders involving white cell lineages
4B0Y Other specified immune system disorders involving white cell lineages
Immune system disorders involving white cell lineages unspecified
ICD 11 Code For Immune system disorders involving white cell lineages unspecified
4B0Z Immune system disorders involving white cell lineages unspecified