Immune System Disorders Involving White Cell Lineages – Definitions & ICD 11 Codes

Coded Elsewhere:

• Immunodeficiencies with predominantly antibody defects (4A01.0)
• Combined immunodeficiencies (4A01.1)
• Defects in the complement system (4A00.1)
• Diseases of immune dysregulation (4A01.2)
• Other well-defined immunodeficiency syndromes due to defects in adaptive immunity (4A01.3)

Disorders of neutrophil number

ICD 11 Code For Disorders of neutrophil number

  4B00  Disorders of neutrophil number

Exclusions:

• Decreased white blood cell count (MA16.10)

4B00.0 Neutropaenia

Coded Elsewhere:

• Transient neonatal neutropaenia (KA8D)

4B00.00 Constitutional neutropaenia

Definition of Constitutional neutropaenia: This is a granulocyte disorder characterised by an abnormally low number of neutrophils. Neutrophils usually make up 50-70% of circulating white blood cells and serve as the primary defence against infections by destroying bacteria in the blood.

Exclusions:

• Cartilage-hair hypoplasia (LD27.0)

4B00.01 Acquired neutropaenia

4B00.0Z Neutropenia unspecified

4B00.1 Neutrophilia

4B00.10 Constitutional neutrophilia

4B00.11 Acquired neutrophilia

Coding Note:

• Code also the causing condition

Exclusions:

• Non mast cell myeloproliferative neoplasms (2A20)

4B00.1Z Neutrophilia unspecified

4B00.Y Other specified disorders of neutrophil number

Disorders of neutrophil function

ICD 11 Code For Disorders of neutrophil function

  4B01  Disorders of neutrophil function

Coded Elsewhere:

• Functional neutrophil defects (4A00.0)

4B01.0 Constitutional disorders of neutrophil function

4B01.00 Disorders of neutrophil adhesion

4B01.01 Disorders of neutrophil chemotaxis

4B01.02 Disorders of neutrophil granule formation or release

4B01.03 Disorders of neutrophil oxidative metabolism

4B01.0Y Other specified constitutional disorders of neutrophil function

4B01.0Z Constitutional disorders of neutrophil function unspecified

4B01.1 Acquired disorders of neutrophil function

4B01.Z Disorders of neutrophil function unspecified

Eosinopenia

ICD 11 Code For Eosinopenia

  4B02  Eosinopenia

4B02.0 Constitutional decrease in eosinophil number

4B02.1 Acquired decrease in eosinophil number

4B02.Z Eosinopenia unspecified

Eosinophilia

ICD 11 Code For Eosinophilia

  4B03  Eosinophilia

4B03.0 Constitutional eosinophilia

4B03.1 Acquired eosinophilia

4B03.Z Eosinophilia unspecified

Disorders with decreased monocyte counts

ICD 11 Code For Disorders with decreased monocyte counts

  4B04  Disorders with decreased monocyte counts

Disorders with increased monocyte counts

ICD 11 Code For Disorders with increased monocyte counts

  4B05  Disorders with increased monocyte counts

Acquired lymphopenia

ICD 11 Code For Acquired lymphopenia

  4B06  Acquired lymphopenia

Acquired lymphocytosis

ICD 11 Code For Acquired lymphocytosis

  4B07  Acquired lymphocytosis

Exclusions:

• Chronic lymphocytic leukaemia or small lymphocytic lymphoma (2A82.0)

Coded Elsewhere:

• Infectious mononucleosis (1D81)

Other specified immune system disorders involving white cell lineages

ICD 11 Code For Other specified immune system disorders involving white cell lineages

  4B0Y  Other specified immune system disorders involving white cell lineages

Immune system disorders involving white cell lineages unspecified

ICD 11 Code For Immune system disorders involving white cell lineages unspecified

  4B0Z  Immune system disorders involving white cell lineages unspecified