ICD 11

Myelodysplastic And Myeloproliferative Neoplasms – Definitions & ICD 11 Codes


Definition of Myelodysplastic And Myeloproliferative Neoplasms: A category of clonal haematopoietic disorders that have both myelodysplastic and myeloproliferative features at the time of initial presentation.

Chronic myelomonocytic leukaemia

Definition of Chronic myelomonocytic leukaemia: A myelodysplastic/myeloproliferative neoplasm which is characterised by persistent monocytosis, absence of a Philadelphia chromosome and BCR/ABL1 fusion gene, fewer than 20 percent blasts in the bone marrow and blood, often myelodysplasia, and absence of PDGFRA or PDGFRB rearrangement.


ICD 11 Codes For Chronic myelomonocytic leukaemia

  2A40  Chronic myelomonocytic leukaemia

Inclusions:

  • Chronic monocytic leukaemia

Exclusions:

Atypical chronic myeloid leukaemia, BCR-ABL1- negative

Definition of Atypical chronic myeloid leukaemia, BCR-ABL1- negative: A myelodysplastic/myeloproliferative neoplasm characterised by the principal involvement of the neutrophil series with leukocytosis with circulating immature myeloid cells, fewer than 20 percent blasts in the bone marrow and blood, and severe dysgranulopoiesis. The neoplastic cells do not have a Philadelphia chromosome or the BCR/ABL1 fusion gene.

ICD 11 Codes For Atypical chronic myeloid leukaemia, BCR-ABL1- negative

  2A41  Atypical chronic myeloid leukaemia, BCR-ABL1- negative

Juvenile myelomonocytic leukaemia

Definition of Juvenile myelomonocytic leukaemia: A myelodysplastic/myeloproliferative neoplasm of childhood that is characterised by proliferation principally of the granulocytic and monocytic lineages. Myelomonocytic proliferation is seen in the bone marrow and the blood. The leukemic cells may infiltrate any tissue, however liver, spleen, lymph nodes, skin, and respiratory tract are the most common sites of involvement.

ICD 11 Codes For Juvenile myelomonocytic leukaemia

  2A42  Juvenile myelomonocytic leukaemia

2A42.0 Juvenile myelomonocytic leukaemia in complete remission

2A42.Y Other specified juvenile myelomonocytic leukaemia

2A42.Z Juvenile myelomonocytic leukaemia unspecified

Refractory anaemia with ring sideroblasts associated with marked thrombocytosis

Definition of Refractory anaemia with ring sideroblasts associated with marked thrombocytosis: A provisional entity that encompasses cases with morphologic and clinical characteristics of refractory anaemia with ring sideroblasts, marked thrombocytosis, and abnormal megakaryocytes.

ICD 11 Codes For Refractory anaemia with ring sideroblasts associated with marked thrombocytosis

  2A43  Refractory anaemia with ring sideroblasts associated with marked thrombocytosis

Myeloproliferative and myelodysplastic disease unclassifiable

Definition of Myeloproliferative and myelodysplastic disease unclassifiable: This entity includes cases that have clinical, laboratory, and morphologic features that support the diagnosis of both a myelodysplastic syndrome and a myeloproliferative neoplasm, but do not meet the criteria for any of the other entities included in the myelodysplastic/myeloproliferative neoplasm category.

ICD 11 Codes For Myeloproliferative and myelodysplastic disease unclassifiable

  2A44  Myeloproliferative and myelodysplastic disease unclassifiable

Other specified myelodysplastic and myeloproliferative neoplasms

ICD 11 Codes For Other specified myelodysplastic and myeloproliferative neoplasms

  2A4Y  Other specified myelodysplastic and myeloproliferative neoplasms

Myelodysplastic and myeloproliferative neoplasms unspecified

ICD 11 Codes For Myelodysplastic and myeloproliferative neoplasms unspecified

  2A4Z  Myelodysplastic and myeloproliferative neoplasms unspecified

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