Definition of Myelodysplastic And Myeloproliferative Neoplasms: A category of clonal haematopoietic disorders that have both myelodysplastic and myeloproliferative features at the time of initial presentation.
Definition of Chronic myelomonocytic leukaemia: A myelodysplastic/myeloproliferative neoplasm which is characterised by persistent monocytosis, absence of a Philadelphia chromosome and BCR/ABL1 fusion gene, fewer than 20 percent blasts in the bone marrow and blood, often myelodysplasia, and absence of PDGFRA or PDGFRB rearrangement.
2A40 Chronic myelomonocytic leukaemia
Definition of Atypical chronic myeloid leukaemia, BCR-ABL1- negative: A myelodysplastic/myeloproliferative neoplasm characterised by the principal involvement of the neutrophil series with leukocytosis with circulating immature myeloid cells, fewer than 20 percent blasts in the bone marrow and blood, and severe dysgranulopoiesis. The neoplastic cells do not have a Philadelphia chromosome or the BCR/ABL1 fusion gene.
2A41 Atypical chronic myeloid leukaemia, BCR-ABL1- negative
Definition of Juvenile myelomonocytic leukaemia: A myelodysplastic/myeloproliferative neoplasm of childhood that is characterised by proliferation principally of the granulocytic and monocytic lineages. Myelomonocytic proliferation is seen in the bone marrow and the blood. The leukemic cells may infiltrate any tissue, however liver, spleen, lymph nodes, skin, and respiratory tract are the most common sites of involvement.
2A42 Juvenile myelomonocytic leukaemia
2A42.0 Juvenile myelomonocytic leukaemia in complete remission
2A42.Y Other specified juvenile myelomonocytic leukaemia
2A42.Z Juvenile myelomonocytic leukaemia unspecified
Definition of Refractory anaemia with ring sideroblasts associated with marked thrombocytosis: A provisional entity that encompasses cases with morphologic and clinical characteristics of refractory anaemia with ring sideroblasts, marked thrombocytosis, and abnormal megakaryocytes.
Definition of Myeloproliferative and myelodysplastic disease unclassifiable: This entity includes cases that have clinical, laboratory, and morphologic features that support the diagnosis of both a myelodysplastic syndrome and a myeloproliferative neoplasm, but do not meet the criteria for any of the other entities included in the myelodysplastic/myeloproliferative neoplasm category.
2A44 Myeloproliferative and myelodysplastic disease unclassifiable
2A4Y Other specified myelodysplastic and myeloproliferative neoplasms
2A4Z Myelodysplastic and myeloproliferative neoplasms unspecified
Definitions of Certain Disorders Involving The Immune System: Disorders in which disturbed immune regulation plays…
Coded Elsewhere: Immunodeficiencies with predominantly antibody defects (4A01.0)Combined immunodeficiencies (4A01.1)Defects in the complement system (4A00.1)Diseases…
Definition of Allergic Or Hypersensitivity Conditions: Allergy is a hypersensitivity reaction initiated by a proven…
Coded Elsewhere: Schnitzler syndrome (EB03) Monogenic autoinflammatory syndromes Definition of Monogenic autoinflammatory syndromes: Monogenic hereditary…
Coded Elsewhere: Rheumatoid arthritis (FA20) Lupus erythematosus Definition of Lupus erythematosus: An autoimmune non-organ specific…
Primary immunodeficiencies due to disorders of innate immunity ICD 11 Codes For Primary immunodeficiencies due…