ICD

Myelodysplastic Syndromes – Definitions & ICD 11 Codes


Definition of Myelodysplastic Syndromes: hematopoietic disorders characterised by dysplasia and ineffective hematopoiesis in one or more of the hematopoietic cell lines. The dysplasia may be accompanied by an increase in myeloblasts, but the number is less than 20% in marrow and blood, which, according to the WHO guidelines, is the requisite threshold for the diagnosis of acute myeloid leukaemia.

Exclusions:


Refractory anaemia

ICD 11 Codes For Refractory anaemia

  2A30  Refractory anaemia

Refractory neutropaenia

Definition of Refractory neutropaenia: A myelodysplastic syndrome characterised by the presence of at least 10% dysplastic neutrophils in the bone marrow or the peripheral blood.

ICD 11 Codes For Refractory neutropaenia

  2A31  Refractory neutropaenia

Refractory thrombocytopenia

Definition of Refractory thrombocytopenia: A myelodysplastic syndrome characterised by the presence of at least 10% dysplastic megakaryocytes, found within at least 30 megakaryocytes examined in the bone marrow.

ICD 11 Codes For Refractory thrombocytopenia

  2A32  Refractory thrombocytopenia

Refractory anaemia with ring sideroblasts

Definition of Refractory anaemia with ring sideroblasts: A myelodysplastic syndrome characterised by an anaemia in which 15% or more of the erythroid precursors are ringed sideroblasts. The ring sideroblast is an erythroid precursor in which one third or more of the nucleus is encircled by granules which are positive for iron stain.

ICD 11 Codes For Refractory anaemia with ring sideroblasts

  2A33  Refractory anaemia with ring sideroblasts

Refractory cytopenia with multi-lineage dysplasia

Definition of Refractory cytopenia with multi-lineage dysplasia: A myelodysplastic syndrome characterised by bi-cytopenia or pancytopenia and dysplastic changes in 10% or more of the cells in two or more of the myeloid cell lines.

ICD 11 Codes For Refractory cytopenia with multi-lineage dysplasia

  2A34  Refractory cytopenia with multi-lineage dysplasia

Refractory anaemia with excess of blasts

Definition of Refractory anaemia with excess of blasts: A myelodysplastic syndrome characterised by bi-cytopenia or pancytopenia and dysplastic changes in one or multiple lineages, with 5-19% myeloblasts in the bone marrow, 2-19% blasts in the blood, or <20% blasts with the presence of Auer rods.

ICD 11 Codes For Refractory anaemia with excess of blasts

  2A35  Refractory anaemia with excess of blasts

Myelodysplastic syndrome with isolated del(5q)

Definition of Myelodysplastic syndrome with isolated del(5q): A myelodysplastic syndrome characterised by anaemia with or without other cytopenias and/or thrombocytosis and in which the sole cytogenetic abnormality is del(5q). Myeloblasts are <5% in the bone marrow and <1% in the blood.

ICD 11 Codes For Myelodysplastic syndrome with isolated del(5q)

  2A36  Myelodysplastic syndrome with isolated del(5q)

Inclusions:

  • 5 q- syndrome

Myelodysplastic syndrome unclassifiable

Definition of Myelodysplastic syndrome unclassifiable: A subtype of myelodysplastic syndrome which at disease presentation lacks findings appropriate for classification into any other MDS category, or has an MDS-associated cytogenetic abnormality and cytopenia, but lack sufficient dysplastic changes in any lineage and have <15% ring sideroblasts.

ICD 11 Codes For Myelodysplastic syndrome unclassifiable

  2A37  Myelodysplastic syndrome unclassifiable

Refractory cytopenia of childhood

Definition of Refractory cytopenia of childhood: The most common subtype of the myelodysplastic syndromes affecting children. It is characterised by persistent cytopenia with less than 5% blasts in the bone marrow and less than 2% blasts in the peripheral blood.

ICD 11 Codes For Refractory cytopenia of childhood

  2A38  Refractory cytopenia of childhood

Other specified myelodysplastic syndromes

ICD 11 Codes For Other specified myelodysplastic syndromes

  2A3Y  Other specified myelodysplastic syndromes

Myelodysplastic syndromes unspecified

ICD 11 Codes For Myelodysplastic syndromes unspecified

  2A3Z  Myelodysplastic syndromes unspecified

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