Polycythaemia – Definitions & ICD 11 Codes

Coded Elsewhere:

  • Polycythaemia vera (2A20.4)

Congenital polycythaemia

Definition of Congenital polycythaemia: A disease caused by determinants occurring in the antenatal period leading to changes in the concentration of red blood cells. This disease is characterised by having a high concentration of red blood cells in the body leading to slow flow of blood. This disease may present with headaches, blurred vision, red skin, tiredness, high blood pressure, dizziness, periods of confusion, bleeding problems gout or itchy skin. Confirmation is by identification of increased levels of red blood cells in a blood sample.

ICD 11 Code For Congenital polycythaemia

  3A80  Congenital polycythaemia

Coded Elsewhere:

  • Polycythaemia neonatorum (KA8A)

3A80.0 Primary inherited erythrocytosis

Definition of Primary inherited erythrocytosis: A disease caused by genetically inherited factors leading to changes in the concentration of red blood cells. This disease is characterised by having a high concentration of red blood cells in the body leading to slow flow of blood. Confirmation is by identification of mutations by genetic testing.

3A80.Y Other specified congenital polycythaemia

3A80.Z Congenital polycythaemia unspecified

Definition of Congenital polycythaemia unspecified: Secondary polycythaemia is acquired and caused by either natural or artificial increases in the production of erythropoietin, hence an increased production of erythrocytes.

Acquired polycythaemia

ICD 11 Code For Acquired polycythaemia

  3A81  Acquired polycythaemia

3A81.0 Polycythaemia due to hypoxia including high altitude

3A81.1 Polycythaemia due to over-transfusion or blood doping

3A81.2 Relative polycythaemia

Definition of Relative polycythaemia: A disease caused by loss of body fluids leading to apparent increased levels of red blood cells in the blood. This disease may present with headache, vertigo, abnormally enlarged spleen or liver, high blood pressure, or formation of blood clots. Confirmation is by identification of relative blood cell counts in a blood sample.

3A81.Y Other specified acquired polycythaemia

3A81.Z Acquired polycythaemia unspecified

Polycythaemia unspecified

ICD 11 Code For Polycythaemia unspecified

  3A8Z  Polycythaemia unspecified

Anaemia due to acute disease

ICD 11 Code For Anaemia due to acute disease

  3A90  Anaemia due to acute disease

Exclusions:

  • Acute posthaemorrhagic anaemia (3A94)

Congenital methaemoglobinaemia

Definition of Congenital methaemoglobinaemia: A disease caused by determinants in the antenatal period leading to lack of the enzyme cytochrome b5 reductase. This disease is characterised by elevated levels of methemoglobin within the blood leading to haemoglobin ineffectively releasing oxygen to body tissues. This disease may present with shortness of breath, cyanosis, headache, fatigue, exercise intolerance, dizziness and loss of consciousness. Confirmation is by identification of mutation by genetic testing.

ICD 11 Code For Congenital methaemoglobinaemia

  3A91  Congenital methaemoglobinaemia

Hereditary methaemoglobinaemia

Definition of Hereditary methaemoglobinaemia: Hereditary methemoglobinemia (HM) is a rare red cell disorder classified principally into two clinical phenotypes: autosomal recessive congenital (or hereditary) methemoglobinemia types I and II (RCM/RHM type 1; RCM/RHM type 2). In RCM type 1, well-tolerated cyanosis from birth is the only symptom. RCM type 2, with global loss of Cb5R function, is much more severe; the cyanosis is accompanied by neurological dysfunction (with intellectual deficit, microcephaly, growth retardation, opisthotonus, strabismus and hypertonia), which usually becomes evident during the first four months of life.

ICD 11 Code For Hereditary methaemoglobinaemia

  3A92  Hereditary methaemoglobinaemia

Acquired methaemoglobinaemia

ICD 11 Code For Acquired methaemoglobinaemia

  3A93  Acquired methaemoglobinaemia

Acute posthaemorrhagic anaemia

Definition of Acute posthaemorrhagic anaemia: A disease caused by blood loss such as subsequent to trauma. This disease is characterised by loss of blood from the body leading to low levels of red blood cells/blood in the body. This disease may present with pallor, fatigue, or shortness of breath. Confirmation is by identification of low levels of red blood cells in a blood sample.

ICD 11 Code For Acute posthaemorrhagic anaemia

  3A94  Acute posthaemorrhagic anaemia

Exclusions:

  • congenital anaemia from fetal blood loss (KA8C)
  • Anaemia due to acute disease (3A90)

Other specified anaemias and erythrocyte disorders

ICD 11 Code For Other specified anaemias and erythrocyte disorders

  3A9Y  Other specified anaemias and erythrocyte disorders

Anaemias or other erythrocyte disorders unspecified

ICD 11 Code For Anaemias or other erythrocyte disorders unspecified

  3A9Z  Anaemias or other erythrocyte disorders unspecified

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