Syphilis (Related Diseases) – ICD 10 & ICD 11 Codes

A predominantly sexually transmitted infection caused by Treponema pallidum ssp. pallidum.

Congenital Syphilis

Definition of Congenital syphilis: A disease caused by an infection with the gram-negative bacteria Treponema pallidum pallidum in utero. This disease may present with clinical signs depending on the stage of disease. Transmission is by vertical transmission.

ICD 11 Code For Congenital Syphilis

1A60 Congenital syphilis

1A60.0 Early congenital syphilis, symptomatic

Definition of Early congenital syphilis, symptomatic: A disease affecting newborns or children up to 2 years of age, caused by an infection with the gram-negative bacteria Treponema pallidum pallidum in utero. This disease is characterised by premature birth, hepatosplenomegaly, skeletal abnormalities, and bullous skin disease. Transmission is by vertical transmission.

1A60.1 Early congenital syphilis latent

1A60.2 Late congenital syphilitic oculopathy

Definition of Late congenital syphilitic oculopathy: This is a late congenital, sexually transmitted infection caused by the spirochete bacterium Treponema pallidum subspecies pallidum. This diagnosis is with oculopathy.

1A60.3 Late congenital neurosyphilis

Definition of Late congenital neurosyphilis: Neurological sequelae of longstanding (> 2 years) untreated congenital neurosyphilis include mental delay, hydrocephalus, seizures, cerebral infarction and cranial nerve palsies.

1A60.4 Other late congenital syphilis, symptomatic

1A60.5 Late congenital syphilis, latent

1A60.Z Congenital syphilis unspecified

ICD 10 Code For Congenital Syphilis

A50 Congenital syphilis

A50.0 Early congenital syphilis, symptomatic

Definition of Early congenital syphilis, symptomatic: Any congenital syphilitic condition specified as early or manifest less than two years after birth. Early congenital syphilis:

• cutaneous
• mucocutaneous
• visceral

Early congenital syphilitic:

• laryngitis
• oculopathy
• osteochondropathy
• pharyngitis
• pneumonia
• rhinitis

A50.1 Early congenital syphilis latent

Definition of Early congenital syphilis, latent: Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after birth.

A50.2 Early congenital syphilis,unspecified

Definition of Early congenital syphilis, unspecified: Congenital syphilis NOS less than two years after birth.

A50.3 Late congenital syphilitic oculopathy

Definition of Late congenital syphilitic oculopathy: Late congenital syphilitic interstitial keratitis, Late congenital syphilitic oculopathy NEC

Exclusions:

• Hutchinson triad

A50.4 Late congenital neurosyphilis [juvenile neurosyphilis]

Dementia paralytica juvenilis Juvenile:

• general paresis
• tabes dorsalis
• taboparetic neurosyphilis

Late congenital syphilitic:

• encephalitis
• meningitis
• polyneuropathy

Use additional code, if desired, to identify any associated mental disorder.

Exclusions:

• Hutchinson triad

A50.5 Other late congenital syphilis symptomatic

Definition of Other late congenital syphilis, symptomatic: Any congenital syphilitic condition specified as late or manifest two years or more after birth.

Clutton joints

Hutchinson:

• teeth
• triad

Late congenital:

• cardiovascular syphilis
• syphilitic:
  – arthropathy
  – osteochondropathy

Syphilitic saddle nose

A50.6 Late congenital syphilis latent

Definition of Late congenital syphilis, latent: Congenital syphilis without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after birth.

A50.7 Late congenital syphilis unspecified

Definition of Late congenital syphilis, unspecified: Congenital syphilis NOS two years or more after birth.

A50.9 Congenital syphilis, unspecified

Early Syphilis

Definition of Early syphilis: A disease caused by an infection with the gram-negative bacteria Treponema pallidum pallidum, including primary and secondary stages of syphilis, and early latent syphilis of less than 2 years duration. This disease is characterised by a single chancre in the primary stage, and diffuse rash in the secondary stage. Transmission is commonly by sexual contact.

ICD 11 Code For Early Syphilis

1A61 Early syphilis

Exclusions:

• Early congenital syphilis

1A61.0 Primary genital syphilis

Definition of Primary genital syphilis A disease caused by an infection with the gram-negative bacteria Treponema pallidum pallidum. This disease is characterised by a single chancre in the genital region. Transmission is commonly by sexual contact.

1A61.1 Primary anal syphilis

1A61.2 Primary syphilis of other sites

1A61.3 Secondary syphilis of skin or mucous membranes

Definition of Secondary syphilis of skin or mucous membranes: A disease caused by an infection with Treponema pallidum pallidum. This disease is characterised by lesions of the skin and mucous membranes. Transmission is commonly by sexual contact.

1A61.4 Secondary syphilis of other sites

Definition of Secondary syphilis of other sites: A disease caused by an infection with the gram-negative bacteria Treponema pallidum pallidum. This disease is characterised by less common symptoms of syphilis, including hepatitis, kidney disease, arthritis, periostitis, optic neuritis, uveitis, or interstitial keratitis. Transmission is commonly by sexual contact.

1A61.5 Latent early syphilis

Definition of Latent early syphilis: A disease caused by an infection with the gram-negative bacteria Treponema pallidum pallidum. This disease is characterised by serologic proof of infection without symptoms of disease less than 1 year after secondary syphilis. Transmission is commonly by sexual contact.

1A61.Y Other specified early syphilis

1A61.Z Early syphilis, unspecified

ICD 10 Code For Early Syphilis

A51 Early syphilis

A51.0 Primary genital syphilis

• Syphilitic chancre NOS

A51.1 Primary anal syphilis

A51.2 Primary syphilis of other sites

A51.3 Secondary syphilis of skin and mucous membranes

Condyloma latum Syphilitic:

• alopecia
• leukoderma
• mucous patch

A51.4 Other secondary syphilis

Secondary syphilitic:

• female pelvic inflammatory disease
• iridocyclitis
• lymphadenopathy
• meningitis
• myositis
• oculopathy NEC
• periostitis

A51.5 Early syphilis, latent

• Syphilis (acquired) without clinical manifestations, with positive serological reaction and negative spinal fluid test, less than two years after infection.

A51.9 Early syphilis, unspecified

Late Syphilis

Definition of Late syphilis: A disease caused by an infection with the gram-negative bacteria Treponema pallidum pallidum. This disease is characterised by gummas, neurological abnormalities, or cardiac abnormalities. Clinical signs normally manifest approximately 3-15 years after initial infection. Transmission is commonly by sexual contact.

ICD 11 Code For Late Syphilis

1A62 Late syphilis

Exclusions:

• Late congenital syphilis

1A62.0 Neurosyphilis

Definition of Neurosyphilis: A disease of the brain or spinal cord caused by an infection with the gram-negative bacteria Treponema pallidum pallidum. This disease is characterised by four different forms: meningovascular, tabes dorsalis, general paresis, or may be asymptomatic. Clinical signs normally manifest approximately 4-25 years after initial infection. Transmission is commonly by sexual contact.

1A62.00 Asymptomatic neurosyphilis

1A62.01 Symptomatic late neurosyphilis

Definition of Symptomatic late neurosyphilis: A diverse constellation of neuropsychiatric signs resulting from prolonged untreated or inadequately treated syphilis. The protean clinical manifestations include chronic, insidious meningeal inflammation with cranial nerve palsy, cognitive and/or behavioural impairment, ataxia, stroke, seizures and visual or auditory impairment.

Coded Elsewhere:

• Dementia due to neurosyphilis
• Meningitis due to Treponema pallidum

1A62.0Z Neurosyphilis, unspecified

1A62.1 Cardiovascular late syphilis

Definition of Cardiovascular late syphilis: This is a late, sexually transmitted infection caused by the spirochete bacterium Treponema pallidum subspecies pallidum. This diagnosis is involving the cardiovascular area.

1A62.2 Symptomatic late syphilis of other sites

1A62.20 Ocular late syphilis

Definition of Ocular late syphilis: This is a late, sexually transmitted infection caused by the spirochete bacterium Treponema pallidum subspecies pallidum. This diagnosis is with ocular.

1A62.21 Late syphilis involving the musculoskeletal system

Definition of Late syphilis involving the musculoskeletal system: This is a late, sexually transmitted infection caused by the spirochete bacterium Treponema pallidum subspecies pallidum. This diagnosis is involving the musculoskeletal system.

1A62.22 Late syphilis of skin or mucous membranes

Definition of Late syphilis of skin or mucous membranes: This is a late, sexually transmitted infection caused by the spirochete bacterium Treponema pallidum subspecies pallidum. This diagnosis is involving the skin and mucous membranes.

1A62.2Y Symptomatic late syphilis of other specified sites

1A62.2Z Symptomatic late syphilis of unspecified site

1A62.Y Other specified late syphilis

1A62.Z Late syphilis, unspecified

ICD 10 Code For Late syphilis

A52 Late syphilis

A52.1 Symptomatic neurosyphilis

Late syphilitic:

• acoustic neuritis
• encephalitis
• meningitis
• optic atrophy
• polyneuropathy
• retrobulbar neuritis

Syphilitic parkinsonism
Syphilitic (tabetic) arthropathy
Tabes dorsalis

Exclusions:

• Charcot arthropathy

A52.2 Asymptomatic neurosyphilis

A52.3 Neurosyphilis, unspecified

• Glomerular disease in syphilis of central nervous system NOS
• Syphilis (late) of central nervous system NOS
• Syphiloma of central nervous system NOS

A52.7 Other symptomatic late syphilis

• Glomerular disease in syphilis any sites, except those classified to A52.0-A52.3
• Gumma (syphilitic) any sites, except those classified to A52.0-A52.3
• Late or tertiary syphilis any sites, except those classified to A52.0-A52.3

Late syphilitic:

• bursitis
• chorioretinitis
• episcleritis
• female pelvic inflammatory disease
• leukoderma
• oculopathy NEC
• peritonitis

Syphilis [stage unspecified] of:

• bone
• liver
• lung
• muscle
• synovium

A52.8 Late syphilis, latent

Definition of Late syphilis, latent: Syphilis (acquired) without clinical manifestations, with positive serological reaction and negative spinal fluid test, two years or more after infection.

A52.9 Late syphilis, unspecified

Latent Syphilis, Unspecified As Early Or Late

Definition of Latent syphilis, unspecified as early or late: disease caused by an infection with the gram-negative bacteria Treponema pallidum pallidum. This disease is characterised by serologic proof of infection without symptoms of disease. Transmission is commonly by sexual contact.
Inclusions: Positive serological reaction for syphilis

ICD 11 Code For Latent Syphilis, Unspecified As Early Or Late

1A63 Latent syphilis, unspecified as early or late

ICD 10 Code For Latent Syphilis, Unspecified As Early Or Late

A53.0 Latent syphilis, unspecified as early or late

• Latent syphilis NOS
• Positive serological reaction for syphilis

Syphilis, Unspecified

ICD 11 Code For Syphilis, Unspecified

1A6Z Syphilis, unspecified

ICD 10 Code For Syphilis, Unspecified

A53.9 Syphilis, unspecified

• Infection due to Treponema pallidum NOS
• Syphilis (acquired) NOS

Exclusions:

• Syphilis NOS causing death under two years of age.